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Joint Bone Spine
Volume 78, n° 1
pages 85-87 (janvier 2011)
Doi : 10.1016/j.jbspin.2010.07.015
accepted : 20 July 2010
Case reports
Unusual multicentric angiomyolipoma of knee joint and soft tissue foot
 

Manish Kumar Varshney a, ⁎ , Manjula Jain b, Alok Sud a, Savita Agarwal b, Manupriya Nain b
a Department of Orthopaedics, Lady Hardinge Medical College and associated hospitals, Connaught Place, Opposite Shivaji Stadium, 110001 New Delhi, India 
b Department of Pathology, Lady Hardinge Medical College and associated Hospitals, 110001 New Delhi, India 

Corresponding author. Tel.: +91 11 23408317; fax: +91 11 23408317.
Abstract

To report unusual occurrence of angiomyolipoma at intraarticular location with another lesion in the same side foot. A 12-year-old girl was referred to us after initial inconclusive work-up done elsewhere for swelling of left knee joint. There was a 15×12cm swelling in the knee joint partially encasing patella while also a similar hourglass shaped swelling measuring 9×4cm was noted in the same side foot. After clinical and radiological evaluation an excision biopsy was planned for both sites. The specimen sent for histopathological evaluation revealed angiomyolipoma with identical characteristics in the two locations and was HMB45 immunostain negative. Patient was evaluated for possibility of tuberous sclerosis but there was no contributory evidence. Angiomyolipoma is typically a solitary renal tumor with rare occurrence at musculoskeletal sites. Multicentric variety is still infrequent. Intraarticular occurrence of angiomyolipoma presents a diagnostic challenge not only in terms of unfamiliarity but also unusual presentation with absence of characteristic immunostaining and multicentricity requiring careful exclusion of other lesions that may require a more radical approach for treatment.


Keywords : Extrarenal angiomyolipoma, PEComas, Musculoskeletal tumors


OutlineMasquer le plan
Introduction
Case report
Discussion
Conflict of interest statement
Ethical board review and consent


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