Primary immunodeficiency update : Part II. Syndromes associated with mucocutaneous candidiasis and noninfectious cutaneous manifestations - 17/08/15
Abstract |
Several primary immunodeficiencies (PIDs) have recently been described that confer an elevated risk of fungal infections and noninfectious cutaneous manifestations. In addition, immunologic advances have provided new insights into our understanding of the pathophysiology of fungal infections in established PIDs. We reviewed PIDs that present with an eczematous dermatitis in part I. In part II of this continuing medical education article we discuss updates on PIDs associated with fungal infections, their biologic basis in PIDs, and noninfectious cutaneous manifestations.
Le texte complet de cet article est disponible en PDF.Abbreviations used : ADA, AIRE, AML, APECED, APLAID, APS-1, AR, CARD9, CLEC7A, CMC, COL1A1-PDGFB, CXCL12, CXCR4, DFSP, DOCK8, EBV, GATA2, GOF, HPV, HSCT, IL, MDS, MonoMAC, MST1, mTEC, NIH, NF-κB, NK, OS, PAMPs, PID, PLAID, PLCG2, PRR, RAG, SCID, SDF-1, STAT3, Treg, TLR, TNF, WHIM, WILD
Plan
Supported by the Intramural Research Program of the National Institutes of Health, Center for Cancer Research, National Cancer Institute. |
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Conflicts of interest: None declared. |
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Date of release: September 2015 |
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Expiration date: September 2018 |
Vol 73 - N° 3
P. 367-381 - septembre 2015 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
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