Acquired cutis laxa associated with heavy chain deposition disease - 01/11/17
Abstract |
Acquired cutis laxa (generalized acquired elastolysis) is a condition of unknown etiology characterized by a degeneration of elastic fibers in the skin, resulting in laxity with reduced elastic recoil. We describe a patient with acquired cutis laxa associated with an underlying heavy chain deposition disease. Direct immunofluorescence testing of lesional skin demonstrated immunoglobulin G deposition on elastic fibers, suggesting that in some cases, cutis laxa may have an immune-mediated etiopathogenesis.
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Conflicts of interest: None declared. |
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Vol 59 - N° 5S
P. S99-S101 - novembre 2008 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
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