Aggressive subcutaneous panniculitis-like T-cell lymphoma with hemophagocytosis in two children (subcutaneous panniculitis-like T-cell lymphoma) - 07/08/11
Abstract |
Subcutaneous panniculitis-like T-cell lymphoma is an uncommon form of cutaneous lymphoma in the pediatric population. It is characterized histologically by subcutaneous infiltration of pleomorphic cytotoxic T cells, mimicking a lobular panniculitis. Although usually described as having an indolent clinical course, the condition may be complicated by systemic involvement and hemophagocytic syndrome, resulting in a poorer prognosis. We present two pediatric patients with aggressive forms of subcutaneous panniculitis-like T-cell lymphoma complicated by hemophagocytic syndrome, and discuss the current literature.
Le texte complet de cet article est disponible en PDF.Key words : ⍺/β, T cells, chemotherapy, cytophagic histiocytic panniculitis, hemophagocytic syndrome, subcutaneous panniculitis-like T-cell lymphoma
Abbreviations used : CHOP, CHP, SPTCL
Plan
Funding sources: None. |
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Conflicts of interest: None declared. |
Vol 61 - N° 5
P. 875-881 - novembre 2009 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
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