Persistent agmination of lymphomatoid papulosis: An equivalent of limited plaque mycosis fungoides type of cutaneous T-cell lymphoma - 19/08/11
Abstract |
Background |
Lymphomatoid papulosis (LyP) is a self-healing eruption in the spectrum of CD30+ lymphoproliferative disorders. The most common lymphoproliferative disorder associated with LyP is the most common form of cutaneous T-cell lymphoma: mycosis fungoides.
Objective |
We sought to describe a distinct entity on the spectrum of CD30+ lymphoproliferative disorders.
Results |
Seven patients presented with similar findings. Within a well-circumscribed area, the size and location of a patch of mycosis fungoides, these patients had continual eruptions of papulonodules that were histologically typical of LyP. The localized areas of involvement were treated as oligolesional mycosis fungoides and long-standing remissions occurred even after years of experiencing continuous localized eruptions. The clinical and histologic findings are reviewed and presented in a way to further the identification of patients with this entity.
Limitations |
This distinct entity is only defined by 7 patients.
Conclusion |
The agmination of LyP-like papulonodules confined to a discrete circumscribed area is a distinct clinical subset within the spectrum of CD30+ lymphoproliferative disorders. The behavior of this entity is that of a progressive lymphoma that warrants therapy.
Le texte complet de cet article est disponible en PDF.Abbreviations used : ALCL, CT, CTCL, LyP, MF
Plan
Funding sources: None. |
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Conflicts of interest: None declared. |
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Reprints not available from the authors. |
Vol 57 - N° 6
P. 1005-1011 - décembre 2007 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
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