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Journal of the American Academy of Dermatology
Volume 42, n° 5P2
pages 907-913 (mai 2000)
Doi : 10.1016/S0190-9622(00)90270-6
Congenital and childhood dermatofibrosarcoma protuberans: A case report and review of the literature

Scott R. Checketts, MD, Tiffani K. Hamilton, MD, Richard D. Baughman, MD
Department of Internal Medicine Section of Dermatology, Dartmouth Hitchcock Medical Center. Lebanon, New Hampshire 


Dermatofibrosarcoma protuberans (DFSP) occurs most commonly on the trunk, affects all races, and often develops between the second and fifth decades of life. It is uncommon in childhood and is sometimes mistaken for a vascular lesion, as it often presents as a blue macule or small nodule. Review of the English literature revealed approximately 152 cases of DFSP developing before 16 years of age and only 19 claimed congenital cases. A case of congenital dermatofibrosarcoma protuberans is presented with a literature review and discussion of congenital and childhood presentations of the tumor. (J Am Acad Dermatol 2000;42:907-13.)

The full text of this article is available in PDF format.

 This supplement is made possible through an educational grant from Ortho Dermatological to the American Academy of Dermatology.
 Reprint requests: Scott R. Checketts, MD, Tanner Memorial Clinic, 2121 N 1700 W, Layton, UT 84041.

*  *References 6, 9, 30, 39, 63, 65, 75, 77, 78, 79, 80, 81, 82, 83
*  *Since the submission of this article, approximately 2 more congenital and 9 to 10 childhood cases of DFSP have been reported.

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