Scleromyxedema with dermato-neuro syndrome - 05/09/11
Doi : 10.1016/S0190-9622(00)90274-3
Joselyn Gonzalez, MDa,b, Mark Palangio, MSc, Joseph Schwartz, MDa, Albert S. Klainer, MDb,c, Emil Bisaccia, MDa,d
Morristown, New Jersey, and New York, New York
From the Section of Photopheresisa and Department of Internal Medicine,b Morristown Memorial Hospital, and the Departments of Medicinec and Dermatology,d Columbia University College of Physicians and Surgeons, New York
Abstract |
Scleromyxedema is a rare connective tissue disease of unknown cause characterized by a generalized papular eruption, dermal fibroblast proliferation, and monoclonal paraproteinemia. A paroxysmal triad consisting of high fever, seizures, and coma with a flu-like prodrome can rarely occur in patients with scleromyxedema and is termed “dermato-neuro syndrome.” We describe a 41-year-old patient with scleromyxedema in whom the dermato-neuro syndrome developed. (J Am Acad Dermatol 2000;42:927-8.)
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 | This supplement is made possible through an educational grant from Ortho Dermatological to the American Academy of Dermatology. |
| Reprint requests: Emil Bisaccia, MD, Morristown Memorial Hospital, 100 Madison Ave, Morristown, NJ 07962-1956. |
© 2000
American Academy of Dermatology, Inc. Publié par Elsevier Masson SAS. Tous droits réservés.
Vol 42 - N° 5P2
P. 927-928 - mai 2000 Retour au numéro
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