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Journal of the American Academy of Dermatology
Volume 58, n° 3
pages 499-502 (mars 2008)
Doi : 10.1016/j.jaad.2007.03.028
Case Reports

Keratosis follicularis spinulosa decalvans in a family
 

Jane S. Bellet, MD a, Andrew L. Kaplan, MD c, M. Angelica Selim, MD b, Elise A. Olsen, MD a,
a Department of Medicine, Division of Dermatology, Duke University Medical Center, Durham, North Carolina 
b Department of Pathology, Duke University Medical Center, Durham, North Carolina 
c Philadelphia Institute of Dermatology, Fort Washington, Pennsylvania 

Correspondence to: Elise A. Olsen, MD, Duke University Medical Center, Box 3294, Durham, NC 27710.
Abstract

Keratosis follicularis spinulosa decalvans (KFSD) is a rare condition characterized by diffuse keratosis pilaris with a scarring alopecia of the scalp and associated photophobia, facial erythema, and palmoplantar keratoderma. Although initially described as a sex-linked disorder, several different inheritance patterns have been observed. We describe a patient whose father and sister were also affected with this condition, consistent with an autosomal dominant genetic transmission. Multiple topical and systemic treatments have been unsuccessful in this patient, attesting to the treatment refractoriness typically seen in KFSD.

The full text of this article is available in PDF format.

 Funding sources: None.
 Conflicts of interest: None declared.
 Reprints not available from the authors.



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