Partially involuting congenital hemangiomas: A report of 8 cases and review of the literature - 18/12/13
Abstract |
Background |
Congenital hemangiomas have been divided into 2 major subtypes based on clinical behavior: rapidly involuting congenital hemangioma (RICH) and noninvoluting congenital hemangioma (NICH).
Objective |
We describe a clinical subtype of congenital hemangioma that begins as a RICH but fails to completely involute and persists as a NICH-like lesion. We propose the term “partially involuting congenital hemangioma” for this lesion with overlapping features.
Methods |
A review of the medical charts, serial clinical photographs, imaging, and biopsies performed on children with a diagnosis of partially involuting congenital hemangioma between 2001 and 2012 at Centre Hospitalier Universitaire Sainte-Justine pediatric dermatology/vascular anomalies clinic was performed.
Results |
Eight full-term, healthy infants presented at birth with vascular lesions typical of RICH. Affected locations included the head and neck, trunk, or extremities. Size varied from 2.0 × 1.5 cm to 13.0 × 8.5 cm. All had rapid involution during the first 12 to 30 months of life before stabilizing in size and appearance.
Limitations |
Only a small number of cases were identified.
Conclusion |
Partially involuting congenital hemangiomas are congenital hemangiomas with a distinct behavior, evolving from RICH to persistent NICH-like lesions. Their recognition and study will help us better understand whether RICH and NICH are indeed separate entities or simply part of a spectrum.
Le texte complet de cet article est disponible en PDF.Key words : infantile hemangioma, noninvoluting congenital hemangioma, partially involuting congenital hemangioma, rapidly involuting congenital hemangioma
Plan
Funding sources: None. |
|
Conflicts of interest: None declared. |
Vol 70 - N° 1
P. 75-79 - janvier 2014 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
L’accès au texte intégral de cet article nécessite un abonnement.
Déjà abonné à cette revue ?