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Joint Bone Spine
Volume 73, n° 3
pages 318-320 (mai 2006)
Doi : 10.1016/j.jbspin.2005.05.004
Received : 23 November 2004 ;  accepted : 14 May 2005
Amyopathic dermatomyositis
 

Bouchra Saoud, Fadoua Allali , Najia Hajjaj Hassouni
Rheumatology B Department, El Ayachi Hospital, Rabat-Salé Teaching Hospitals, Rabat-Salé, Morocco 

*Corresponding author. Tel.: +21 261 181 824.
Abstract

Amyopathic dermatomyositis (ADM) is a rare condition characterized by skin lesions suggestive of dermatomyositis (DM) without detectable muscle abnormalities after at least 2 years of follow-up. Pulmonary fibrosis is uncommon in patients with ADM.

Case report. - A 64-year-old woman presented with a 2 years and 6 months history of nondestructive polyarthritis. She had skin changes suggestive of DM, including a pink rash over the face, neck, and forearms; Gottron's papules over the metacarpophalangeal joints; and heliotrope edema of the eyelids. She reported no muscle symptoms. Findings were normal from muscle enzyme assays, electromyography, and muscle biopsies. A diagnosis of ADM was given. Early lung fibrosis was found. Investigations for a tumor were negative.

Discussion. - ADM is a rare condition that may be an abortive form of DM with a favorable outcome and a lower risk of malignancy compared to classic DM. However, the development of pulmonary fibrosis may cloud the prognosis.

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Keywords : Amyopathic dermatomyositis, Pulmonary fibrosis




© 2005  Elsevier SAS. All Rights Reserved.