Constriction Band Syndrome - 20/08/11

Doi : 10.1016/j.hcl.2008.10.007

Kenji Kawamura, MD, PhD ^a, Kevin C. Chung, MD ^b,^⁎
^a Department of Orthopaedic Surgery, Nara Medical University, 840 Shijyo-cho, Kashihara, Nara 634-8522, Japan
^b Section of Plastic Surgery, Department of Surgery, University of Michigan Medical School, 2130 Taubman Center, 1500 E. Medical Center Drive, Ann Arbor, MI 48109-0340, USA

Corresponding author.

Abstract

Constriction band syndrome is an uncommon congenital abnormality with multiple disfiguring and disabling manifestations. Early amnion rupture with subsequent entanglement of fetal parts by amniotic strands is currently the primary theory for the development of this syndrome. Management of constriction band syndrome is focused on improving function and development while providing a more acceptable esthetic appearance. The treatment should be tailored to the individual. Timing of repair and surgical planning are important to provide the best functional results for affected hands.

El texto completo de este artículo está disponible en PDF.

Keywords : Constriction band syndrome, Malformation, Congenital anomaly, Hand, Treatment

Esquema

Epidemiology and etiology

Clinical presentation

Release of Constriction Bands

Surgery for Acrosyndactyly

Reconstruction for Digital Hypoplasia and Amputation

Summary

Supported in part by a Midcareer Investigator Award in Patient-Oriented Research (K24 AR053120) from the National Institute of Arthritis and Musculoskeletal and Skin Diseases (to Kevin C. Chung).