46-XY Denys-Drash Syndrome. Is There a Role for Nephron-sparing Modalities in Management of Renal Masses? A Report of 2 Cases - 18/06/18
Doi : 10.1016/j.urology.2018.04.023
Amr Hodhod * 
, Mohamed El-Sherbiny
, Mohamed El-Sherbiny Department of Pediatric Surgery, McGill University, The Montreal Children's Hospital, Montréal, Quebec, Canada
*Address correspondence to: Amr Hodhod, M.D., Department of Pediatric Surgery, McGill University, The Montreal Children's Hospital, Room B04.2916.1 GLEN, 1001 Boulevard Décarie, Montréal, Quebec, Canada H4A 3J1.Department of Pediatric SurgeryMcGill University, The Montreal Children's HospitalRoom B04.2916.1 GLEN, 1001 Boulevard DécarieMontréalQuebecH4A 3J1Canada
Abstract |
Denys-Drash syndrome (DDS) is a combination of genital and urinary anomalies that are mostly associated with renal and gonadal malignancies. We report 2 patients who presented with genital ambiguity and were diagnosed as 46-XY DDS. Both patients had renal masses during follow-up and underwent partial nephrectomy aiming to have transplant at older age.
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| Financial Disclosure:The authors declare that they have no relevant financial interests. |
© 2018
Elsevier Inc. Tous droits réservés.
Vol 117
P. 153-155 - juillet 2018 Retour au numéro
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