Postoperative pneumothorax after nephrectomy in a patient with tuberous sclerosis and undiagnosed lymphangioleiomyomatosis - 02/03/22

Highlights |
• | Before surgery in a patient with known tuberous sclerosis (TS) and particularly of genetic origin in a young woman, lymphangioleiomyomatosis (LAM) should be evoked. |
• | Its diagnosis should be ensured before proceeding to surgery to avoid the risk of respiratory complications including pneumothorax. |
• | In patients with a known combination of LAM and TS, anesthetic and surgical management is aimed to reduce both LAM-associated risk (i.e. respiratory complications) and TS-associated risk (neurological, cardiac and renal involvement). |
Keywords : Lymphangioleiomyomatosis, Tuberous sclerosis, General anesthesia, Pneumothorax, Protective ventilation
Vol 78
Article 110655- juin 2022 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
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