Lymphangioma in the bladder is extremely rare. An 8-year-old girl presented with a terminal hematuria associated with intermitted fever. Ultrasonography, computed tomogram, and retrograde urethrography showed a mass that was in the wall of the bladder. The tumor was red and found to be bulging into the bladder on the right lateral wall of the bladder by cystoscopy. A partial cystectomy was performed and histology revealed a lymphangioma of the bladder. The patient was followed up for 3 years with no evidence of recurrence. This case, to the authors' knowledge, represents the third reported case of lymphangioma of bladder.Lymphangiomas are benign, soft-tissue tumors of lymphatic origin. They rarely affect the urinary system and a location in the bladder is extremely rare. Only 2 cases of lymphangioma of the bladder have been reported worldwide since 1983. The present report describes a patient with a lymphangioma of the bladder and the imaging characteristics of the lesion are reported, including imagings of sonography, computed tomography, retrograde urethrography, and histologic examination.