Chronic Inflammatory Demyelinating Polyneuropathy and Variants - 27/10/25
, Richard J. Barohn, MD b, Jonathan S. Katz, MD c, Mazen M. Dimachkie, MD dRésumé |
Chronic inflammatory demyelinating polyradiculoneuropathy (CIDP) is the prototypic chronic inflammatory polyneuropathy, characterized by well-defined clinical and electrodiagnostic criteria, despite the absence of biomarkers or full understanding of disease pathogenesis. It has both a typical form and 5 variants. IVIG remains the treatment of choice for induction or maintenance of remission, although corticosteroids, plasma exchange, and most recently, efgartigimod, demonstrate therapeutic efficacy. Subcutaneous immunoglobulin is indicated only as maintenance therapy. Validated outcome measures exist to track disability, strength, and quality of life and should be routinely employed in clinical practice.
Le texte complet de cet article est disponible en PDF.Keywords : CIDP, CIDP variants, Multifocal acquired demyelinating sensory and motor (MADSAM) neuropathy, Electrodiagnostic demyelinating criteria, CIDP treatment
Plan
Vol 43 - N° 4
P. 761-780 - novembre 2025 Retour au numéroBienvenue sur EM-consulte, la référence des professionnels de santé.
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