Bladder agenesis is a rare congenital anomaly infrequently reported in the literature, with an incidence of 1/600,000 patients.<sup>1Glenn JF. Agenesis of the bladder J Am Med Assoc 1959 ;  169 : 2016-2018 [cross-ref]

Cliccare qui per andare alla sezione Riferimenti</sup> Commonly associated with other fatal malformations, the condition is often incompatible with life.<sup>2Frimberger D, Kropp BP. Bladder anomalies in childreneditors. Campbell-walsh Urology : Saunders-Elsevier (2007).  3573-3583

Cliccare qui per andare alla sezione Riferimenti</sup> Prior reports estimate that over 90% of living children born with this malformation are female, owing to renal preservation resulting from low pressure drainage of urine into the vagina, uterus, and vestibule.<sup>3Graham SD. Agenesis of bladder J Urol 1972 ;  107 : 660-661 [cross-ref]

Cliccare qui per andare alla sezione Riferimenti,4Indiran V, Chokkappan K, Gunaseelan E. Rare case of urinary bladder agenesis–multislice CT abdomen imaging J Radiol Case Rep 2013 ;  7 (2) : 44-4910.3941/jrcr.v7i2.1326Published 2013 Feb 1.

Cliccare qui per andare alla sezione Riferimenti</sup> Herein we report a rare case of an infant male born with penoscrotal transposition and end stage renal disease secondary to bilateral cystic renal dysplasia found to have concurrent bladder agenesis and bilateral ureteral ectopia.